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Int. braz j urol. vol.34 número3

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Congenital Megaprepuce: A New Alternative Technique for

Surgical Correction

Jovelino Q. Leao, Luiz G. Freitas Filho, Adriano L. Gomes, Antonio C. Heinsich, Jose Carnevale

Division of Urology (JQL, LGFF, ALG, ACH, JC), Darcy Vargas Children’s Hospital, Sao Paulo, and Division of Pediatric Surgery (LGFF), Federal University of Sao Paulo, Sao Paulo, Brazil

ABSTRACT

Objective:To present a new alternative technique for surgical treatment of congenital megaprepuce.

Materials and Methods: )URP$SULOWR$SULO¿YHSDWLHQWVDJHGWR\HDUVZHUHWUHDWHGXVLQJWKHQHZWHFKQLTXH 7KHWHFKQLTXHLVGHVFULEHGDQGLOOXVWUDWHG,WGLIIHUVIURPRWKHUWHFKQLTXHVLQWKDWLWWDNHVLQWRFRQVLGHUDWLRQWKHFRQVWDQW EDOORRQLQJRIWKHIRUHVNLQZKLFKJLYHVWRWKHH[WHUQDOJHQLWDOLDWKHDVSHFWRIDSHQRVFURWDOWUDQVSRVLWLRQ&RVPHWLFDQG IXQFWLRQDOVXFFHVVZHUHDOVRDVVHVVHGE\DFDVHUHYLHZ

Results:$IWHUDIROORZXSRIWR\HDUVDOOSDWLHQWVKDYHQRUPDOYRLGLQJDQGDVDWLVIDFWRU\FRVPHWLFDVSHFW Conclusion:7KLVQHZWHFKQLTXHFRXOGEHDXVHIXODOWHUQDWLYHLQWUHDWPHQWRIWKHFRQJHQLWDOPHJDSUHSXFH

Key words: penis; children; foreskin; congenital abnormalities; surgery

Int Braz J Urol. 2008; 34: 313-8

INTRODUCTION &RQJHQLWDOPHJDSUHSXFHLVDPDOIRUPDWLRQ FRQVLVWLQJRIDJUHDWUHGXQGDQF\RIWKHLQQHUSUHSXWLDO VNLQRYHUDQRUPDOSHQLOHVKDIWDQGJODQV7KHSUHSXFH LVQRWUHWUDFWDEOHDQGDEDOORRQLQJRIWKHIRUHVNLQLV SURGXFHGGXULQJWKHPLFWXULWLRQ,WZDV¿UVWGHVFULEHG E\2¶%ULHQHWDOLQDQGVLQFHWKHQRWKHU DXWKRUVKDYHVKRZQWKDWDOWKRXJKDUDUHFRQGLWLRQ LWLVRIWHQFRQIXVHGZLWKEXULHGWUDSSHGFRQFHDOHG ZHEEHGRUPLFURSHQLV 7KHH[XEHUDQWLQQHUSUHSXFHFORVHGE\WKH SUHSXWLDOULQJFUHDWHVDUHVHUYRLUZLWKDODUJHGLPHQ -VLRQOHDGLQJWRWKHDQDWRPLFDODVSHFWRISHQRVFURWDO WUDQVSRVLWLRQ)LJXUHDQG&RPSUHVVLRQRIWKH SHQLOHVKDIWUHVXOWVLQXULQHVSLOODJH)LJXUH7KH GLDJQRVLVLVPDGHWKHUHIRUHHVVHQWLDOO\E\SK\VLFDO H[DPLQDWLRQZKLFKGRHVQRWUHTXLUHIXQFWLRQDOH[ -SORUDWLRQ 7KHREMHFWLYHRIWKLVUHSRUWZDVWRSUHVHQW

D QHZ DOWHUQDWLYH VXUJLFDO WHFKQLTXH WKDW WDNHV LQ account the penoscrotal transposition aspect of the PDOIRUPDWLRQZKLFKSHUPLWVDVDWLVIDFWRU\FRVPHWLF appearance.

MATERIALS AND METHODS

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Congenital Megaprepuce: Surgical Correction

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Figure 1 – The arrow shows an aspect of penoscrotal transposi-tion in a patient with megaprepuce.

Figure 2 – Typical penoscrotal ballooning of the congenital megaprepuce.

Figure 3 – 7KH DUURZ VKRZV WKH XULQDU\ MHW ÀRZ ZKHQ WKH foreskin is squeezed.

RESULTS

$OOSDWLHQWVSUHVHQWHGZLWKWKHGLDJQRVLVRI EXULHGSHQLVDQGRXWRIKDYHKDGUHSHDWHGXULQDU\ tract infections. After the surgical treatment all pa-WLHQWVKDYHQRUPDOYRLGLQJSDWWHUQDQGWKHFRVPHWLF DVSHFWZDVFRQVLGHUHGDGHTXDWHWR\HDUVDIWHU VXUJHU\)LJXUHDQG

COMMENTS

&RQJHQLWDOPHJDSUHSXFHZDV¿UVWGHVFULEHG E\2¶%ULHQHWDO,WLVFDXVHGE\DUHGXQGDQWLQQHU SUHSXFHRYHUDSUHSXWLDOULQJZKLFKLVQRWUHWUDFWDEOH OHDGLQJWRDEDOORRQLQJRIWKHIRUHVNLQ&KURQLFDOO\ LW FUHDWHV D UHVHUYRLU ZKLFK UHQGHUV WKH H[WHUQDO genitalia an aspect of a penoscrotal transposition.

,QDJUHHPHQWZLWKRWKHUDXWKRUVZHEHOLHYH

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Figure 5 – Traction in the ventral preputial ring changing the broken incision into a strait line.

Figure 4 – A) Correction o penoscrotal transposition. B) Sche-matic drawing. Arrows show the lateral incisions.

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Congenital Megaprepuce: Surgical Correction

8QOLNHRWKHUSXEOLVKHGVHULHVDOORXUSDWLHQWV EXWRQHSUHVHQWHGZLWKDXULQDU\WUDFWLQIHFWLRQ

Figure 6 – A) Cutting the inner prepuce. B) Schematic draw-ing.

Figure 7 – Stitches incorporate the foreskin to the penile shaft.

$VUHSRUWHGE\6XPPHUWRQHWDOZHGLV

-DJUHHZLWK3RSLVDQG&UDSSWKDWHDUO\FLUFXPFLVLRQ FXUHVWKHSUREOHPEHFDXVHWKLVZRXOGUHPRYHWKH EDVLFVNLQUHTXLUHGWRUHVXUIDFHWKHSHQLOHVKDIW 7KHVXUJLFDOWHFKQLTXHSUHVHQWHGLQWKLVVWXG\ LVDLPHGDWFRUUHFWLQJWKHSHQRVFURWDOWUDQVSRVLWLRQ LQDGGLWLRQWRWKHUHVHFWLRQRIWKHUHGXQGDQWLQQHU prepuce.

$OWKRXJKWKHSUHVHQWVHULHVLQFOXGHGRQO\¿YH SDWLHQWVZHEHOLHYHDVLQWKHVHULHVRI6XPPHUWRQHW DOWKDWZKHQWKHLPPHGLDWHSRVWRSHUDWLYHDVSHFW LVFRVPHWLFDOO\WUHDWHGWKHORQJWHUPUHVXOWVZLOOEH VDWLVIDFWRU\

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CONFLICT OF INTEREST

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REFERENCES

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-JHQLWDOPHJDSUHSXFH3HGLDWU6XUJ,QW 4.

6XPPHUWRQ'-0F1DOO\-'HQQ\$-0DORQH36 &RQJHQLWDOPHJDSUHSXFHDQHPHUJLQJFRQGLWLRQKRZ WRUHFRJQL]HDQGWUHDWLW%-8,QW Figure 9 – Postoperative aspect 18 months after surgical cor-rection.

Figure 8 – A) and B) Postoperative surgical aspect.

A

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Congenital Megaprepuce: Surgical Correction

'HOJDGR2'RPLQJXH]+6HUUDQR'(VWRUQHOO0 0DUWLQH]9*DUFLD,0HJDSUHSXFLRFRQJHQLWRGLDJ -QRVWLFR\PDQHMRWHUDSHXWLFR$FWDV8URO(VS

3KLOLS,1LFKRODV-/&RQJHQLWDOJLDQWSUHSXFLDOVDF FDVHUHSRUWV-3HGLDWU6XUJ

)HUUR)6SDJQROL$6S\ULGDNLV,$W]RUL30DUWLQL /%RUVHOOLQR$6XUJLFDODSSURDFKWRWKHFRQJHQLWDO PHJDSUHSXFH-3ODVW5HFRQVWU$HVWKHW6XUJ

3RZLV05&DSSV63UHSXWLDOLQWXVVXVFHSWLRQRUDFTXLUHG PHJDSUHSXFH3HGLDWU6XUJ,QW

Accepted after revision: December 11, 2007

Correspondence address:

Imagem

Figure 3 –  7KH DUURZ VKRZV WKH XULQDU\ MHW ÀRZ ZKHQ WKH foreskin is squeezed.
Figure 5 – Traction in the ventral preputial ring changing the  broken incision into a strait line.
Figure 6 – A) Cutting the inner prepuce. B) Schematic draw- draw-ing.
Figure 8 – A) and B) Postoperative surgical aspect.

Referências

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