[PDF] Top 20 Enzyme replacement therapy for Fabry disease: a systematic review and meta-analysis

... for Fabry disease (FD) is enzyme replacement therapy (ERT) with agalsidase alfa or ...A systematic review and meta-analysis was conducted to assess ... See full document

... -Fabry disease (AFd) is a rare disorder characterised by the deficiency or absence of lysosomal enzy- ... See full document

... for Fabry disease as compared to other disorders, we applied it to a total of 412 previously analyzed urine probes from female patients suffering from a wide variety of renal, metabolic and ... See full document

... Fabry disease is an X-linked glycosphingolipid storage disorder caused by a deficiency in the activity of the lysosomal hydrolase a-galactosidase A ...cardiac and cerebrovascular disease. The ... See full document

... this meta-analysis demonstrated that combined inhibition therapy yielded a statistically significant benefit in PFS as compared with single inhibition ...VEGFR and EGFR signaling pathways ... See full document

... this review, the determined heterogeneity is a mix of bias and the threshold effect, as the ELISA tests thresholds are estimated using internal controls by a variety of criteria, and its values may ... See full document

... patterns and other patient support ...previous systematic reviews [4, 68] of observational studies, this review observed a significant heterogeneity in study ...sensitivity analysis by ... See full document

... falls and other conditions were evaluated in patients with Parkinson ’s ...] and Loureiro [ 26 ], in experimental studies without a com- parison group, concluded that training using the Nintendo Wii Fit ... See full document

... Science and Technology Periodical Database (VIP), and Chinese Biomedical Literature Database ...groups: disease (sudden sensorineural hearing loss and other related terms); in- tervention ... See full document

... designs and limitations embodied in the following aspects: (1) Randomiza- tion All selected trials demonstrated ...[25,40], and sealed envelopes ...Placebo and Blind- ing Fourteen studies did not use ... See full document

... A study 32 has suggested that subgroups of IBD patients, such as younger patients, high baseline IBD activity, recently diagnosed individuals, poor coping and high anxiety/depression symptoms, could benefit more ... See full document

... angiotensin-converting enzyme inhibitors (ACEi) and angiotensin-receptor blockers (ARB) facilitate the inoculation of potentially leading to a higher risk of infection and/or disease ... See full document

... (2017) analysis was to evaluate the efficacy and safety of ERT for AFD, in our opinion, the authors used an inappro- priate methodological approach that does not allow conclu- sions to be drawn about the ... See full document

... LILACS, and Biological Abstracts); (ii) hand-searching of specialist journals (journals most likely to contain surveys in this area have been searched such as Am J Public Health, Addic- tion, Tob Control, MMWR ... See full document

... diagnosis, and the specific aspects of children are discussed within the text, such as limit-setting and sleep-onset association issues ...psychotherapy, and pharma- cological ...frequency and ... See full document

... non-commercially, and license their derivative works on different terms, provided the original work is properly cited, appropriate credit is given, any changes made indicated, and the use is ... See full document

... Bickel and colleagues in 1951 ...understood, and the use of unpalatable low-Phe protein hydrolysates with inadequate nutritional composition resulted in poor adherence and unfavorable outcomes ... See full document

... Thinking and feeling, on the other hand, take place at a conscious level and correspond to the subjective experi- ence of ...(DIF) and describing feelings (DDF) accompa- nied by an external oriented ... See full document

... relux disease (GERD) in the population, there is much controversy in this topic, especially in the surgical ...total and partial fundoplication. Data sources - A systematic review of the ... See full document

... smoking and the occurrence of IM in human adults; (3) exposure defined as smoking cigarettes, pipes, bidis or cigars; and (4) outcome defined as intestinal metaplasia of the stomach, excluding the cardia, as ... See full document