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Wegener Granulomatosis

Cranial Nerve Injury as an Initial Sign of Wegener Granulomatosis: Misdiagnosis and Fatal Course in Two Cases

Cranial Nerve Injury as an Initial Sign of Wegener Granulomatosis: Misdiagnosis and Fatal Course in Two Cases

... the Wegener granulomatosis, and it’s typically characterized by a necrotizing granulomatous vasculitis of the respiratory tracts, kidneys, and ...in Wegener granulomatosis ranges from 22% to ...

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Testicular Involvement in Wegener Granulomatosis: Case Report and Review of the literature

Testicular Involvement in Wegener Granulomatosis: Case Report and Review of the literature

... Wegener granulomatosis (WG) is a type of necrotising vasculitis that affects mainly the respiratory tract, paranasal sinuses and the kidneys (1). It mostly presents with nonspecific symptoms in whites ...

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EULAR/PRINTO/PRES criteria for Henoch-Schonlein purpura, childhood polyarteritis nodosa, childhood Wegener granulomatosis and childhood Takayasu arteritis: Ankara 2008. Part II: Final classification criteria

EULAR/PRINTO/PRES criteria for Henoch-Schonlein purpura, childhood polyarteritis nodosa, childhood Wegener granulomatosis and childhood Takayasu arteritis: Ankara 2008. Part II: Final classification criteria

... Objectives To validate the previously proposed classifi cation criteria for Henoch–Schönlein purpura (HSP), childhood polyarteritis nodosa (c-PAN), c-Wegener granulomatosis (c-WG) and c-Takayasu arteritis ...

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Int. Arch. .  vol.19 número3

Int. Arch. . vol.19 número3

... Objective To describe a case of Wegener disease with atypical manifestation. Resumed Report We describe the case of a 50-year-old woman with chronic otitis media and sensorineural hearing loss as the primary ...

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Clinical features of childhood granulomatosis with polyangiitis (wegener's granulomatosis)

Clinical features of childhood granulomatosis with polyangiitis (wegener's granulomatosis)

... 16. Ruperto N, Ozen S, Pistorio A, Dolezalova P, Brogan P, Cabral DA, Cuttica R, Khubchandani R, Lovell DJ, O'Neil KM, Quartier P, Ravelli A, Iusan SM, Filocamo G, Magalhaes CS, Unsal E, Oliveira S, Bracaglia C, Bagga A, ...

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Granulomatose de Wegener: relatos de casos.

Granulomatose de Wegener: relatos de casos.

... Wegener granulomatosis (WG) is characterized by a classic triad of granulomatous inflammation of the respiratory tract, necrotizing vasculitis and ...

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Fulminant Wegener's granulomatosis: A case report

Fulminant Wegener's granulomatosis: A case report

... Wegener granulomatosis (WG) is anti-neutrophil cyto- plasmic antibodies (ANCAs)-associated systemic vasculitis of small arteries and veins of unknown ...

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Neuropatia vasculítica na granulomatose de Wegener: relato de caso.

Neuropatia vasculítica na granulomatose de Wegener: relato de caso.

... during Wegener granulomatosis reachs 15-50% of patients, however as initial symptomatology is not commented in the ...Wegener’s granulomatosis and mononeuritis multiplex, emphasizing the fact that ...

2

Otite Média refratária como primeira manifestação de Granulomatose de Wegener

Otite Média refratária como primeira manifestação de Granulomatose de Wegener

... 2. Vanessa ER, Hwang PH. Wegener’s granulomatosis: current trends in diagnosis and management. Curr Opin Otolaryngol Head Neck Surg. 2007; 15:170-6. 3. Rasmussen N. Management of the ear, nose, and throat ...

1

Manifestação otológica localizada em paciente com granulomatose de Wegener.

Manifestação otológica localizada em paciente com granulomatose de Wegener.

... 4. Furtado RN, Maia MB, Azevedo E, Franco M, Andrade LE: Com- prometimento renal e ocular como manifestações iniciais de granu- lomatose de Wegener. Rev Bras Reumatol 37 (6): 343-7, 1997. 5. Thornton MA, ...

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Granulomatose de Wegener e estenose subglótica: descrição de caso .

Granulomatose de Wegener e estenose subglótica: descrição de caso .

... with Wegener Granulomatosis being treated with steroids and cyclofosfamide that developed progressive dyspnea and hoarseness despite of ...with Wegener granulomatosis and subglottic ...

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REPORT OF THE CASES Patient 1

REPORT OF THE CASES Patient 1

... 12. Campbell H, Escudier MP, Brostoff J, Patel P, Milligan P, Challacombe SJ, et al. Dietary intervention for oral allergy syndrome as a treatment in orofacial granulomatosis: A new approach? J Oral Pathol Med. ...

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J. bras. pneumol.  vol.31 número4

J. bras. pneumol. vol.31 número4

... de Wegener é uma doença multissistêmica caracterizada na histologia por inflamação granulomatosa e vasculite que acomete, na maioria dos casos, o trato respiratório e os ...de Wegener e acometimento ...

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Granulomatose de Wegener Intolerante a Ciclofosfamida tratada com sucesso com Micofenolato Mofetil.

Granulomatose de Wegener Intolerante a Ciclofosfamida tratada com sucesso com Micofenolato Mofetil.

... Cyclophosphamide (CYC) is a classical drug for the treatment of severe Wegener´s granulomatosis (WG). However, as it causes substantial toxicity, al- ternative agents should be considered if optimal ...

5

Pseudotumor esclerosante de órbita.

Pseudotumor esclerosante de órbita.

... de Wegener, sinusite, tu- berculose orbitária, carcinoma metástatico, meningeoma, linfoma e Síndrome de Ormond (fibroesclerose multifocal envolvendo órbita, retroperitôneo e tireoide) (5) ...

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Silent acute myocarditis in eosinophilic granulomatosis with polyangiitis

Silent acute myocarditis in eosinophilic granulomatosis with polyangiitis

... Eosinophilic granulomatosis with polyangiitis is a rare multisystemic disorder, characterized by necrotizing vasculitis affecting small to medium-sized vessels, as- sociated with asthma and ...eosinophilic ...

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Perfuração do septo nasal: etiologia e diagnóstico.

Perfuração do septo nasal: etiologia e diagnóstico.

... A biópsia é de extrema importância no diagnóstico etiológico da perfuração septal e deve ser realizada na investigação inicial. Além de excluir ou confirmar a presença de neoplasias como o carcinoma epidermoide (27), faz ...

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Mastoidite e paralisia facial como manifestações iniciais de Granulomatose de Wegener.

Mastoidite e paralisia facial como manifestações iniciais de Granulomatose de Wegener.

... de Wegener com envolvimento otológico apresenta otite média serosa por disfunção da tuba auditiva. O acometimento primário da cavidade nasal e seios paranasais com inflamação da nasofaringe é o mecanismo proposto ...

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Mastoidite e paralisia facial como manifestações iniciais de Granulomatose de Wegener

Mastoidite e paralisia facial como manifestações iniciais de Granulomatose de Wegener

... This paper aims to offer an update on the possible early isolated clinical manifestations of ear injury con- nected to Wegener’s granulomatosis. The cases of three patients diagnosed with Wegener’s ...

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Acometimento orbitário na doença de Rosai-Dorfman.

Acometimento orbitário na doença de Rosai-Dorfman.

... pseudotumor orbitário e xantogranuloma é possível atra- vés das análises histológica e imuno-histoquímica e tam- bém pela presença de dor mais frequente no pseudotumor orbitário. Nos casos de acometimento da órbita ...

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