772 Letter to the Editor
International Braz J Urol Vol. 34 (6): 772-773, November - December, 2008
Childhood Renal Lymphangiectasia
To the Editor,
An asymptomatic 4 month-old white female had a 2 x 3 cm faint birthmark on her mid-thoracic back consistent with a cutaneous telangiectasia. MRI
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lesion in the enlarged right kidney and proximal ip-silateral ureter as well as heterogeneously increased renal cortical echogenicity. Abdominal CT scan
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circumscribing the right kidney and proximal ureter
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heterogenously hyperintense and hypointense on
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with a renal lymphangiectasia. At 2.5 years of follow-up, she remains asymptomatic without radiological change.
Renal lymphangiectasia is a rare, benign
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be focal, unilateral or bilateral and may be found in pediatric or adult patients. There are reports of familial
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lymphangiectasia can appear suddenly, grow rapidly,
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pain, abdominal pain/distension, palpable abdominal
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773 Letter to the Editor
mass, lower extremity edema and hypertension. Renal
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diagnosis, including renal US, IVP, CT, and MRI. Renal US can show an enlarged and lobulated kidney with increased echogenicity and loss of normal
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show hyperintensity of the renal parenchyma espe-cially at the cortical region and hypointensity at the medullary region. Also, multiple hyperintense lesions in perirenal spaces on T2-weighted images can be appreciated. Pediatric differential diagnosis includes polycystic renal disease, urinoma, renal lymphoma
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imaging is characteristic.
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enteral medium chain triglycerides may be indicated
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suggest that asymptomatic patients with unchanged cystic lesions on US do not require follow-up, we feel patients should undergo lifelong follow-up as occasionally renal function will deteriorate.
REFERENCES
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Fabian Sanchez, Juan C. Prieto, Korgun Koral & Linda A. Baker
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